Table 2: Generalized findings associated with XP subtypes [2,6].
XP Subtype | United States Prevalence | Cutaneous Manifestation Severity | Mean Age of BCC | Neurologic Regression Severity |
XPA | 9% | Severe | 9.7 | Mild to Severe |
XPB | 1% | Moderate | - | None to Severe |
XPC | 43% | Moderate | 14.0 | Absent |
XPD | 28% | Moderate | 38.0 | None to Severe |
XPE | 3% | Mild | 38.3 | Absent |
XPF0% | 0% | Mild | 43.7 | None or Severe |
XPG | 3% | Moderate | 32.0 | None or Severe |
XPV | 7% | Mild | 41.5 | Absent |