Table 1: Patients who underwent a neurosurgical procedure prior to develop CAA and/or iCJD.

Author

Age

Sex

Presentation

Documented Dural Graft (cadaveric or synthetic)

Neurosurgical Procedure

Interval of Years from the Surgery to the Illness

Genetics:

APP,

PSEN1, PSEN2

Genetics:

APOEε

Ehling [9]

38

M

CAA

No

TBI

> 20

NM

ε3/ε3

Purruker [11]

37

M

CAA

No

TBI

> 20

NM

NA

Purruker [11]

42

M

CAA

No

TBI

40

NM

NA

Frontzek

28

M

iCJD + CAA

Yes

TBI

21

NM

NA

Frontzek [8]

33

F

iCJD + CAA

Yes

TBI

25

NM

NA

Frontzek [8]

47

M

iCJD + CAA

Yes

TBI

21

NM

NA

Frontzek [8]

51

M

iCJD

Yes

Not specified

12

NM

NA

Frontzek [8]

52

F

iCJD + CAA

Yes

Pituitare adenoma

22

NM

NA

Nakayama [7]

32

M

CAA

No

TBI

31

NM

ε3/ε3

Jaunmuktane [2]

39

F

CAA

No

TBI

36

NM

ε3/ε4

Jaunmuktane [8]

31

M

CAA

No

Brain tumor

30

NM

ε2/ε3

Jaunmuktane [8]

36

F

CAA

No

Craneofacial malformations

35

NM

ε3/ε4

Hervé [1]

46

F

CAA

Yes

TBI

44

NM

ε2/ε3

Cali [12]

26

M

iCJD

Yes

Not specified

19

NM

NA

Cali [12]

39

F

iCJD

Yes

Not specified

6

NM

NA

Cali [12]

32

M

iCJD

Yes

Not specified

16

NM

NA

Cali [12]

25

M

iCJD

Yes

Not specified

8

NM

NA

Cali [12]

29

M

iCJD

Yes

Not specified

25

NM

NA

Cali [12]

42

M

iCJD

Yes

Not specified

6

NM

NA

Cali [12]

50

F

iCJD

Yes

Not specified

11

NM

NA

Cali [12]

23

F

iCJD

Yes

Not specified

21

NM

NA

Cali [12]

26

F

iCJD

Yes

Not specified

12

NM

NA

Cali [12]

42

M

iCJD

Yes

Not specified

18

NM

NA

Banerjee [5]

48

M

CAA

Yes

Brain tumor

37

NM

ε3/ε3

Banerjee [5]

39

M

CAA

Yes

Cavernous hemangioma embolization

37

NM

ε2/ε3

Banerjee [5]

34

F

CAA

Yes

TBI

34

NM

ε3/ε3

Hamaguchi [6]

30

M

CAA

No

TBI

30

NM

ε3/ε3

Hamaguchi [6]

30

M

CAA

No

TBI

30

NM

ε3/ε3

Giaccone [10]

29

M

CAA

No

TBI

28

NM

NA

NA = Not Available; TBI= Trauma Brain Injury; CAA = Cerebral Amyloid Angiopathy ; CJD= Creuzfelt-Jakob Disease, NM = No Mutations