Table 2: Patients with proven or highly probable FVII Padua (Arg304Gln) reported in North-Central and South America.

Authors (year) Proven Homozygote or Comp. Het. Proven Heterozygote Probable Homozygote Probable Heterozygote Countries Comments
Triplet, et al. [3] n.r. n.r. 4 n.r. USA African-Americans one patient had venous thrombosis
Sabharwal, et al. [14] 1 n.r. n.r. n.r. USA African-American; patient had venous thrombosis
Shurafa, et al. [15] 1 n.r. n.r. n.r. USA African-American
Kuppuswamy, et al. [9] 1 n.r. n.r. n.r. USA a) Ethnic background unspecified; comp. het. with Gln100Arg
Krauss, et al. [14] n.r. n.r. 2 n.r. USA African-Americans
Rodriguez, et al. [13] None 3 n.r. n.r. Brazil Ethnic background undetermined
Barnett, et al. [17] n.r. n.r. 1 n.r. USA African-American
Pollak, et al. [4] 1 3 a) n.r. n.r. USA African-Americans a) 1 patient was compound het. With Arg315Trp
Herrmann, et al. [8] None 5 a) n.r. n.r. Costa Rica, Venezuela, USA a) 4 Het. and 1 compound het. With Gly365Cys (USA). Ethnic group undetermined
Kirkel, et al. [5] 1 None n.r. n.r. USA African-American
Rabelo, et al. [10] 3 1 n.r. n.r. Brazil Ethnic group undetermined
Girolami, et al. [11] 1 1 n.r. n.r. Argentina Caucasian
Girolami, et al. [12] 1 1 n.r. n.r. Argentina Caucasian