Table 1: Summary of patients in the literature review.

N

Authors and year

Country

Age/Gender

Clinical picture

Pulmonary pressure

Medical treatment

Surgical treatment

Evolution

1

Tsutsumi,  et al.,/1992 [6]

Japan

24 yrs/F

Dyspnoea and chest pain

95 mmHg

Not applicable

Operated

Favourable

2

Uehara, et al.,/2007 [7]

Japan

5 months/F

Cyanosis

Not applicable

Not applicable

Operated

Favourable

3

Tanoue, et al.,/2008 [8]

Japan

24 days

Dyspnoea

Not applicable

Not applicable

Operated

Favourable

4

Yang, et al.,

/2012 [9]

South

Korea

27y/M

Chest discomfort

Not applicable

Antiplatelet agents

Not applicable

Favourable

5

Sahai, et al.,/2022 [10]

India

01years/M

Systolic murmur

+ thrill

Normal

Not applicable

Not applicable

Favourable

6

Kishore, et al.,/2024 [11]

India

20 yrs/F

Systolic murmur

40 mmHg

Not applicable

Operated

Favourable

7

Nacanabo, et al.,/2025

Burkina

Faso

27 yrs/M

Syncope, dyspnoea, collapse

56 mmHg

Diuretic, vasopressor amine

No

Died